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Hemophagocytosis in the acute phase of fatal Kawasaki disease in a 4 month-old girl

Balkan Medical Journal · Temmuz 2016

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YÖKSİS Kayıtları
Hemophagocytosis in the Acute Phase of Fatal Kawasaki Disease in a 4 Month Old Girl
Balkan Medical Journal · 2016 SCI-Expanded
PROFESÖR RESUL YILMAZ →

Makale Bilgileri

DergiBalkan Medical Journal
Yayın TarihiTemmuz 2016
Cilt / Sayfa33 · 470-472
Erişim🔓 Açık Erişim
Özet Background: Kawasaki disease is a systemic vasculitis predominately affecting coronary arteries. Hemophagocytic lymphohistiocytosis can complicate the course of Kawasaki disease. Rare cases of secondary hemophagocytic lymphohistiocytosis occurring during the acute phase of Kawasaki disease have been reported. Case Report: We report here a 4 month-old girl with diffuse coronary ectasia and secondary hemophagocytic lymphohistiocytosis occurring during the acute phase of incomplete Kawasaki disease. Conclusion: Due to the large overlap in clinical symptoms, the presence of atypical findings for Kawasaki disease should suggest the possible diagnosis of hemophagocytic lymphohistiocytosis in these patients.

Yazarlar (5)

1
Vehbi Doğan
2
Erhan Karaaslan
3
Samet Özer
ORCID: 0000-0003-0880-7215
4
Ruveyda Gumuser
5
Resul Yilmaz

Anahtar Kelimeler

Coronary artery dilatation Hemophagocytic lymphohistiocytosis Kawasaki disease Macrophage activation syndrome

Kurumlar

Dr. Sami Ulus Maternity and Children Research and Training Hospital
Ankara Turkey
Tokat Gaziosmanpaşa Üniversitesi
Tokat Turkey

Metrikler

10
Atıf
5
Yazar
4
Anahtar Kelime

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